University of the french west indies, actes laboratory. Yet, the orthopedic manifestations of the syndrome are unique. Scribd is the worlds largest social reading and publishing site. Macrodactylie isolee secondaire a une mutation activatrice. The full text of this article is available in pdf format. Cover photo is available under public domain license. Proteus syndrome is a rare disorder with a genetic background that can cause tissue overgrowth involving all three embryonic lineages. The clinical and radiographic manifestations of proteus syndrome are highly variable. The first sign is the lack of a growth spurt during the early teen years. The diagnosis of transsexualism was introduced in the dsmiii in 1980 for gender dysphoric individuals who demonstrated at least two years of continuous interest in transforming the sex of.
The syndrome is named after the greek seagod proteus, who could change his shape. Les maladies rares et leurs manifestations cliniques orales dans. A read is counted each time someone views a publication summary such as the title, abstract, and list of authors, clicks on a figure, or views or downloads the fulltext. Il existe une grande heterogeneite clinique des macrodactylies. Constipation et syndrome occlusif en situation palliative. Proteus syndrome is a rare disorder with a genetic background that can cause tissue.1053 357 210 792 1305 483 337 1216 891 1427 352 1217 196 932 866 687 1574 998 860 492 1174 229 42 1475 1262 1296 584 886